Cystic fibrosis

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Cystic fibrosis (CF) affects the lungs, the digestive system, sweat glands and also fertility in males. It causes the lungs and pancreas to make thick mucus, which then clogs ducts and passages in the lungs. These blockages trap bacteria, leading to frequent infections and damage to the lungs. The pancreatic juices needed to properly digest food are also affected, so children with CF sometimes suffer from malnutrition.

CF is the most common life-threatening inherited disease in Australia. Two CF genes, one from each parent, are required to cause this condition. Nowadays, with appropriate treatment, people with cystic fibrosis can live productive lives well into middle age.

Special lung clearance techniques usually need to be performed twice a day. Nutritional supplements, a high-energy diet and enzyme tablets, steroids and antibiotics are also needed.

Children with CF need to stay active and exercise to keep their lungs healthy and build the strength necessary to withstand infections.

A child with CF may miss a lot of school time because of frequent hospital visits, and may be affected by constant wheezing, coughing and other symptoms. It's important to let teachers know about your child's condition and to consult regularly with them.

The following professionals can help: genetic counsellor, paediatrician, respiratory physician, dietitian, physiotherapist.

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